Nutrição e Distrofia Muscular de Duchenne – Intervenção Nutricional

Associados, juntamente com os artigos do mês, vocês receberão uma cartilha resumo com as principais intervenções nutricionais da condição/ doença que é tema do mês! A cartilha resumo poderá ser utilizada como um material de apoio para o momento do atendimento nutricional, facilitando a prescrição de condutas com base nos dados mais recentes dos estudos científicos.

Nutrição e Distrofia Muscular de Duchenne – Artigo 10

The Relationship between Obesity and Clinical Outcomes in Young People with Duchenne Muscular Dystrophy Abstract: Background: Duchenne muscular dystrophy (DMD) is a severe X-linked neuromuscular disorder. Young people withDMDhave high rates of obesity. There is emerging evidence that a higher BMI may negatively affect clinical outcomes in DMD. This study aimed to explore the relationship between obesity and clinical outcomes in DMD. Methods: ...

Nutrição e Distrofia Muscular de Duchenne – Artigo 9

When dysbiosis meets dystrophy: an unwanted gut-muscle connection Duchenne muscular dystrophy (DMD) is a devastating neuromuscular degenerative disease with no known cure to date. In recent years, the hypothesis of a “gutmuscle axis” has emerged suggesting that bidirectional communication between the gut microbiota and the muscular system regulates the muscular function and may be perturbed in several muscular disorders. In addition, the ...

Nutrição e Distrofia Muscular de Duchenne – Artigo 8

A systematic literature review and meta-analysis of the effectiveness of vitamin D supplementation for patients with Duchenne muscular dystrophy A b s t r a c t We conducted a systematic literature review and meta-analysis on the effectiveness of vitamin D supplementation in maintaining or restoring vitamin D levels in Duchenne muscular dystrophy. Due to a lack of randomised controlled trials, cross-sectional and retrospective and prospect...

Nutrição e Distrofia Muscular de Duchenne – Artigo 7

Frequency of Delayed Puberty in Boys with Contemporary Management of Duchenne Muscular Dystrophy Abstract Background: Delayed puberty is thought to be common in boys with Duchenne muscular dystrophy (DMD) treated with long term oral glucocorticoid. This study aims to report the frequency of delayed puberty in DMD from examination by a paediatric endocrinologist alongside detailed endocrine investigations. Methods: All boys with DMD aged at ...

Nutrição e Distrofia Muscular de Duchenne – Artigo 6

Nutritional Issues among Children with Duchenne Muscular Dystrophy—Incidence of Deficiency and Excess Body Mass Abstract: The progression of Duchenne muscular dystrophy (DMD)requires the assessment of nutritional disturbances at each stage of the disease. The purpose of this study was to assess the nutritional status in various ages of boys with DMD using screening and in-depth evaluation methods. Body composition by Dual X-ray Absorptiom...

Nutrição e Distrofia Muscular de Duchenne – Artigo 5

Duchenne muscular dystrophy Abstract Duchenne muscular dystrophy is a severe, progressive, muscle-wasting disease that leads to difficulties with movement and, eventually, to the need for assisted ventilation and premature death. The disease is caused by mutations in DMD (encoding dystrophin) that abolish the production of dystrophin in muscle. Muscles without dystrophin are more sensitive to damage, resulting in progressive loss of muscle ...